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What is Bell's palsy?
Bell's palsy is a form of facial paralysis resulting from damage to
the VIIth (facial) cranial nerve. The condition is named for Sir Charles
Bell, a Scottish surgeon in Edinburgh who studied the nerve and its innervations of the
facial muscles in1821. Since the function of the facial nerve is so complex, many symptoms
may occur when the fibers of the facial nerve are disrupted. A disorder of the facial nerve may
result in twitching, weakness or paralysis of the face, dryness of the eye or the mouth, or in
disturbance of taste.
Bell's Palsy temporarily prevents the nerve from transmitting
signals to the muscles, causing weakness
or paralysis. When half or one side of these individual nerve fibers are interrupted, hemi-facial
weakness occurs. Rarely we see bilateral facial paralysis. If these nerve fibers are irritated, then movements of the facial muscles appear as
spasms or twitching.
It can strike almost anyone at any age. Statistics indicate that the disorder affects approximately 2 out of 10,000 people, however, the actual incidence is likely to be much higher.
The muscles of the eyelid are supplied by
the (facial) VII nerve, but the muscles that control all the eyeball movements (rectus and oblique
muscles) are not. Thus, there will be difficulty in closing the eyelids, but the
vision and the eyeball movements are not affected, as the optic and trochlear
nerves are not involved. The taste sensations are affected, as they are
carried via the facial nerve, but the tongue movements are normal. Skin sensation
over the ear maybe affected with tingling sensation over the rest of the face. Chewing
and swallowing actions are usually normal.
What are the causes for Bell’s palsy?
The specific cause of Bell's Palsy is unknown. A number of things can damage the
facial cranial nerve and lead to Bell's palsy. Several systemic diseases can
cause facial paralysis and are sometimes misdiagnosed as Bell's palsy. Most Bells Palsy are
designated as idiopathic, but it is caused by an inflammation within the small bony tube
called the fallopian canal (in the temporal bone), through which the nerve passes before exiting
from the stylomastoid foramen. The canal is an extremely narrow area, and
an inflammation within it is likely to exert pressure on the nerve. The
nerve has not yet divided into its several branches thus resulting in impairment
of all functions controlled by the VIIth nerve.
It has been suggested by various sources that it may be
associated with the following:
1. Viral and Bacterial infection (about 75% of cases). Viral and Bacterial infections that are said to cause
Bells Palsy are: Herpes simplex virus (HSV-1) has been identified as the most
frequent cause of Bells palsy. A vast majority of the population has been exposed to HSV-1 during
childhood. The active virus produces cold sores (blisters) over the body, but the virus often runs
its course without causing any blisters (blisters actually appear in only 15% of
the cases). HSV-1 is only infectious for a short period of time, after which it
enters into a dormant state. For most people, the virus remains
dormant forever. But sometimes the dormant virus are triggered into its active
form. The triggers for reactivation of the virus is not known. Decreased immunity, stress, lack of
sleep, minor illness, upper respiratory infection, autoimmune syndromes, chronic disease, etc has been
thought to be the causative factor. When this occurs the immune system
automatically begins to produce antibodies to destroy the virus, resulting in an
inflammatory reaction. But the
inflammation occurs in the small tight canal (fallopian canal) with no space for
swelling, thus putting pressure on the nerve and compressing it. Compression of the nerve
stops transmission
of nerve stimuli to the facial muscles, and causes weakened or paralyzed facial
muscles, resulting in Bell's palsy.
Ramsey Hunt Syndrome (RHS) is caused by Varicella Zoster virus
(VSV), the
same virus that causes chicken pox. Like HSV-1,
it remains in the body after the initial infectious stage, residing on nerve tissue
and on nerve
ganglia in a dormant state. The symptom is usually the appearance of
blisters in the ear, which can be expected to last 15-30 days. The blisters can appear prior
to, concurrent to, or even after the onset of facial paralysis. RHS can also affect
the auditory nerve (VIII Cranial nerve). It is contagious and contact with an open blister by someone who has never had chickenpox
can result in transmission of the virus.
HIV can cause Bells Palsy. In the early stages of HIV, paralysis
can be directly related to the viral infection, but in the later stages paralysis is
mainly due to the associated opportunistic infections or tumors.
Cytomegalovirus, Epstein Barr virus etc have also been implicated as the cause for Bells Palsy.
2. Diabetes.
3. Flu-like illness, toxins. Lyme disease can cause symptoms of Bells palsy. Bacteria
may enter the body through the skin at the site of the tick bite and produce flu-like symptoms. Typical early symptom of Lyme disease
is a red ring around the site of the tick bite. Without an
antibiotic therapy the bacteria can spread throughout the body, causing arthritis, heart
disease, and nervous system disorders such as facial paralysis.
4. High blood pressure.
5. Respiratory infection (about 50% of cases).
6. Trauma, temporal bone fractures, trauma to the facial nerve etc.
7. Surgical wounds
8. Brain stem injuries.
9. Cysts and tumors.
10. Guillain-Barre syndrome.
11. Sarcoidosis.
12. Myasthenia Gravis.
13. Sjogrens syndrome.
14. Stress.
15. High winds directly onto the face.
16. Poor nutrition.
17. Dental Treatment.
18. Otitis Media. Bacteria from acute or chronic
middle ear infections can invade the fallopian canal around the nerve. As with viruses, the invasion
can evoke an inflammatory response, and compress the nerve.
19. Pregnancy is not a cause but it's been reported that a high number of pregnant women have
been affected.
20. Venereal diseases.
21. Thyroid malfunctions.
22. Melkersson-Rosenthal syndrome.
23. Kawasaki disease.
24. Multiple sclerosis.
25. Parotitis.
26. It has also been suggested that it can be inherited or due to a congenital defect.
What are the symptoms and the problems associated
with Bell’s palsy?
The VIIth Facial cranial nerve has both motor and sensory functions. Its motor
functions include shutting the eye, lifting the eyebrow, and supplying the
muscles that move the mouth and lips. Its sensory functions include tasting
on the front of the tongue and dampening the level of the sound we hear.
So the symptoms of Bell's palsy include any abnormalities involving these
various muscles. Many people describe feeling a pain behind their ear or
near the jaw a few days before the other symptoms develop. Symptoms begin suddenly and hit their
peak usually within 48 hours. Seventy-five percent of cases are preceded by upper respiratory
infection or a viral infection.
1. The most common symptom of Bell's palsy is weakness on one entire side of the face. Sudden
one-sided facial paralysis or weakness of the facial muscles.
2. A person may not be able to close one eye, inability to blink, or they may have difficulty shutting
their eye completely. Diminished blinking and the absence of tearing together can reduce or eliminate
the flow of tears across the eyeball, resulting in drying, erosion, and ulcer formation on the cornea
and possible loss of the eye.
3. The forehead doesn't wrinkle when a person tries to lift their eyebrow.
4. The lower part of the face may droop down.
5. Patients aren't able to lift their mouths to smile or fill their cheeks with air.
6. They may drool from the mouth.
7. Some people may feel a tingling, twitching or numbness in the face.
8. Face feels stiff or pulled to one side, change in facial appearance, difficulty
with facial expressions, grimacing etc, difficulty with fine facial movements, asymmetrical smile.
9. Dry eyes or tearing (crocodile tears).
10. Pain in the back of the head, ear, behind the ear, or the affected side of the face.
11. Hypersensitivity to sound (hyperacusis) or hearing deficit.
12. Dry mouth and impairment of taste.
13. Difficulty with eating and drinking.
14. Speech is affected.
15. Nose feels stuffed or blocked, or runs.
16. Pain in or near the ear. Blisters in the ear.
17. Fatigue and dizziness (vertigo).
18. Tooth decay and gum disease due to reduced saliva and impairment of chewing.
19. Psychological and self-esteem problems.
What are the Diagnostic tests done?
During the clinical examination you will be asked to do various things
with your face. Your doctor may ask you to lift your eyebrows and then
lower them, close your eyes tightly, wrinkle your forehead, blow out your
cheek, whistle etc if the two sides don't move in the same way, it suggests that
one side is weaker than the other. Not being able to taste on the front
of the tongue and noises sounding louder than expected are both indications
of Bell's palsy. Blood pressure is checked. A skull x-ray may be done to rule-out infection or tumor.
Symptoms of Bell's palsy will appear only in the face,
muscle weakness in other parts of the body suggests that there is some
other problem. After an examination of the head, neck, and ears, a series of tests may be performed.
The most common tests are:
Hearing Test: Determines if the cause of damage to the nerve has involved the hearing nerve,
inner ear, or delicate hearing mechanism.
Balance Test: Evaluates balance nerve involvement.
Tear Test: Measures the eye's ability to produce tears.
Imaging: CT (computerized tomography) or MRI (magnetic resonance imaging) determine if there is
infection, tumor, bone fracture, or other abnormality in the area of the facial nerve.
Electrical Test: Stimulates the facial nerve to assess how badly the nerve is damaged.
This test may have to be repeated at frequent intervals to see if the disease is progressing.
Laboratory or blood studies may be necessary to determine the underlying cause like
autoimmune problems, Lyme disease or other viral infections which can lead
to Bell's palsy.
What is the treatment for Bell’s palsy?
The prognosis for Bell's palsy is generally very good. With or without
treatment, most patients begin to get significantly better within 2 weeks,
and about 80 percent recover completely within 3 months. For some, however,
the symptoms may last longer. In a few cases, the symptoms may never completely
disappear. Only 1 in 10 patients never experience a complete disappearance
of symptoms. The extent of nerve damage determines the extent of recovery.
There is no specific treatment for Bell's palsy.
The most important part of treatment is to keep the eyes healthy and moist. One of the purposes
of blinking and closing the eyes is to keep the eyes wet. If a person can't
close their eyes, because the muscles that control the eyelids are paralyzed,
it is important to keep the eyes moist and prevent itching. Eye drops are
prescribed for the day, and an eye ointment for the night to prevent drying of the surface of the eye
cornea. Diminished blinking and the absence of tearing together can reduce or eliminate the flow of
tears across the eyeball, resulting in drying, erosion, and ulcer formation on the cornea and possible
loss of the eye.
Closing the eye with a finger is an effective way of keeping the eye moist. Use the back of the finger
to ensure that the eye is not injured with the finger tip. Protective glasses or clear eye patches
are often used to keep the eye moist, and to keep foreign materials from entering the eye.
If infection is the cause, then an antibiotic to fight
bacteria (as in middle ear infections) or antiviral agents (to fight syndromes caused by viruses like
HSV, Ramsay Hunt) may be used.
If simple swelling is believed to be responsible for the facial nerve disorder, then
corticosteroids (prednisone) can be administered to relieve swelling and to
prevent an early condition from getting worse. It is usually given
for one week, though it shouldn't be prescribed if there are any signs
of infection or other problems that are known to cause complications with
short-term steroid use. A pain reliever may be necessary to relieve pain.
Some have used electrical
stimulation to stimulate the facial nerve. There is no scientific evidence of its effectiveness. Some researchers
have found that electrical stimulation might have caused further nerve
damage and delayed healing. Sometimes physiotherapy can be helpful in strengthening the facial
muscles. Patients with Bell's Palsy should find ways to reduce the stressful situations in their
lives in order to speed recovery and avoid recurrence.
Massage muscles of the forehead, cheek, lips and eyes using cream or oil. Exercise the weak muscles in front of a mirror. Open and close the eye, wink, smile and bare your teeth. Perform the massage and exercise for 15 or 20 minutes several times a day. Some patients may benefit from a special form of physical therapy called facial retraining. Brush and floss teeth more often to keep the mouth healthy.
Patients with permanent facial paralysis may be rehabilitated through a variety of surgical procedures including eyelid weights or springs, muscle transfers and nerve substitutions. Other medical treatments for complications of facial paralysis including excessive motion of the face (twitching) or muscle spasm may involve surgical division of overactive muscles or weakening them by chemical injection. In certain circumstances, surgical removal of the bone around the nerve (decompression) may be done.
What is Residual Effects (Synkinesis)?
People usually recover completely from Bells Palsy. Generally the regeneration of nerves will
be complete within three months after onset. If recovery is delayed by more than
three months then sometimes you may
begin to notice movements in areas of the face that you are not even trying to
move. This is referred to as Residual Effects (Synkinesis). When you smile the eye may close
or twitch, or when you close you eye the corner of your mouth may pull up or out
to the side. Residual effects is seen only in cases where recovery from Bell's palsy is delayed beyond the 3 months.
The longer the recovery takes beyond the initial three months, the
more severe the residual effects. It is characterized by
uncoordinated or unsynchronized facial movements that occur along with normal
movements. Synkinesis varies in severity from mild to severe.
Synkinesis is theorized to be the effect of abnormal nerve regeneration. Within the main
trunk of the facial nerve are between 6000-7000 different,
very delicate, very thin, frail nerve fibers that conduct the electrical
signal from the brain to the facial muscles. Inflammation within the canal can
cause damage to some of these very frail fibers. In time these damaged nerve fibers
regenerate (at the rate of about 1-2mm per day). But there's no mechanism that
directs these fibers back into their original muscles. Some
of the healing nerve fibers may implant themselves into the
wrong muscles. The brain sends the
signal for the muscle to contract thinking the nerve fiber is still connected to
the original muscle, but instead, the nerve may be lodged in an entirely
different muscle, resulting in movement of a completely different muscle. The affected side of the face may feel
tight as the result of the uncontrolled muscle contractions (spasms).
Treatment for residual Synkinesis can be effective at any time after it is noticed. The focus of the treatment is on re-coordinating the various muscles rather than stimulating them. We know that when Synkinesis is present the facial muscles are viable, or "alive". Even an abnormal movement is still a movement. It is possible to restore more normal movement patterns and expression with specific, appropriate training through physiotherapy.
Conclusion
Disorders of the facial nerve, including paralysis, are not rare and can be due
to a variety of causes.
The appropriate diagnosis and treatment are very important to achieving the best possible recovery of
facial nerve function. Even patients with permanent facial nerve injury can be helped by surgical
procedures designed to improve facial function.
Considerable attention must be given to maintaining a healthy eye, which requires a constant flow of
tears. Brush and floss teeth more often to keep the mouth healthy.
Bell's palsy is distressing, but it is not dangerous. The disorder is not a threat to life.
Most people do not have a recurrence, however, some do.
Some Facts:
1. It is an "equal opportunity" disease. The percentage of left
or right side cases is approximately equal, and remains equal for recurrences.
2. The incidence of Bell's palsy in males and females, as well
as in the various races is also approximately equal.
3. Older people are more likely to be afflicted, but children
are not immune to it. Children tend to recover well.
4. Diabetics are more than 4 times more likely to develop Bells
Palsy than the general population.
5. Conditions that compromise the immune system such as HIV increase
the odds of facial paralysis occurring and recurring.
6. Bilateral Bell's palsy is rare, accounting for less than 1%
of cases.
7. The degree of paralysis should peak within several days of
onset, usually never longer than 2 weeks (3 weeks max for RHS).
8. The nerve regenerates at a rate of approximately 1 millimeter
per day.
9. Approximately 50% of Bells Palsy patients will have essentially
complete recoveries in a short time. Another 35% will have good recoveries
in less than a year.
10. The nerve can continue to regenerate for 18 months, probably even
longer. Improvement of appearance can continue beyond that time frame.
11. The possibility of recurrence had been thought to be as high as
10 - 20%. These figures have been lowered as more has been learned about
the types of facial paralysis that are now known to be other than Bell's
palsy. Estimates of the rate of recurrence still vary widely, from around
4 - 14%.
12. The muscles that close the eyelid are controlled by VII nerve,
but the muscles that control other eye movements and the ability to focus
are not. There will be difficulty in closing the eyelids, but other functions
and movement of the eye is not affected. The sense of taste is affected,
but tongue motion is not. Skin sensation may be affected near the ear,
but sensation over the rest of the face usually remains normal. Chewing
and swallowing are not affected.
13. Various viral infections (herpes, Lyme disease, mumps, tuberculosis,
HIV, etc), tumors, bony abnormalities, a skull fracture or any other trauma,
surgery, neurological dysfunction (diabetes), various neurological disorders
(Guillain-Barre syndrome, myasthenia gravis, etc), micro-circulation problems,
etc can lead to facial palsy.
14. Bell's palsy and Ramsey Hunt syndrome can be bilateral, but it's
rare. Mononucleosis, flu, Guillain-Barre Syndrome, Leukemia, Lyme disease,
Sarcoidosis and Heerdfort's Syndrome can be potential triggers of bilateral
palsy.
15. Residual effects can be present in cases where recovery from Bell's
palsy is delayed beyond the 3 months period.
Dr Antony George, Mani Specialty Dental Clinic,
Pottayil Lane, M.G. Road, Trichur, Kerala 680001, India.
Ph: (91-0487)385996 Fax:0091-0487-384721
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